Authors:

A. Ariputra

Abstract:

“Evans syndrome is a coexistence of simultaneous or sequential positive direct Coombs test in conjunctionwith immune-mediated thrombocytopenia with no known underlying etiology. The clinical course ischronic and relapsing, and the therapy is generally progressive. Recurrences of thrombocytopenia, anemiaand neutropenia are common, as well as episodes of hemorrhage and serious infections. Noncrossreactingautoantibodies are directed against red cells, platelets, and neutrophils antigens. Evans syndrome isa rare condition, no predilection is known and its exact prevalent is unknown. We report a case of Evanssyndrome in 10 years old girl with severe anemia and thrombocytopenia. Patient came with clinicalsymptoms of severe anemia. The laboratory evaluation showed severe anemia, increased reticulocytecount, anisopoikilocytosis erythrocyte, increased unconjugated bilirubin, positive direct Coombs testand thrombocytopenia. Patient was then managed with high doses of corticosteroids and showed goodresponse from both clinical and laboratory evaluations. [MEDICINA 2015;46:61-66].Sindrom Evans adalah suatu penyakit yang ditandai dengan adanya hasil positif pada direct Coombstest dan trombositopenia yang diperantarai imun secara simultan atau sekuensial tanpa penyebabyang jelas. Perjalanan klinis umumnya bersifat kronis, sering mengalami relaps dan memerlukanterapi yang progresif. Kejadian trombositopenia, anemia, neutropenia, perdarahan dan episode infeksiberat berulang umum terjadi. Pada sindrom ini, terjadi reaksi autoantibodi spesifik terhadap antigensel darah merah, trombosit dan juga neutrofil. Sindrom Evans merupakan kasus yang jarang ditemukandan dengan predileksi serta prevalensi yang belum banyak diketahui. Kami melaporkan satu kasusSindrom Evans pada anak perempuan usia 10 tahun. Pasien dengan gejala klinis anemia berat dan padapemeriksaan laboratorium menunjukkan suatu anemia berat, peningkatan hitung retikulosit, gambaraneritrosit anisopoikilositosis, peningkatan kadar bilirubin yang tidak terkonjugasi, direct Coombs test yangpositif dan trombositopenia. Pasien kemudian diterapi dengan kortikosteroid dosis tinggi dandidapatkan respon yang baik pada evaluasi klinis dan laboratorium. [MEDICINA 2015;46:61-66].”

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PDF:

https://jurnal.harianregional.com/medicina/full-15983

Published

2021-11-09

How To Cite

ARIPUTRA, A.. EVANS SYNDROME IN A 10 YEAR OLD GIRL.Medicina, [S.l.], v. 46, n. 1, oct. 2015. ISSN 2540-8321. Available at: https://jurnal.harianregional.com/medicina/id-15983. Date accessed: 08 Jul. 2024.

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Issue

Vol 46 No 1 (2015): Januari 2015

Section

Articles

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